Irsiy progressiv musinozli gistiotsitoz - Hereditary progressive mucinous histiocytosis

Irsiy progressiv musinozli gistiotsitoz
Autosomal dominant - en.svg
Ushbu holat autosomal dominant tarzda meros qilib olinadi
MutaxassisligiDermatologiya

Irsiy progressiv musinozli gistiotsitoz juda kam uchraydigan, benign, Langerhanz bo'lmagan hujayralar gistiotsitozidir. An autosomal dominant yoki X bilan bog'langan teri ustida tasvirlangan irsiy kasallik, deyarli faqat ayollarda topilgan.[1][2] Erkak bemorda kasallikning bitta holati qayd etilgan.[3]

Shuningdek qarang

Adabiyotlar

  1. ^ Jeyms, Uilyam D.; Berger, Timoti G.; va boshq. (2006). Endryusning teri kasalliklari: klinik dermatologiya. Sonders Elsevier. pp.718. ISBN  978-0-7216-2921-6.
  2. ^ Antoni-Bax, N; Pfister, R; Grosshans, E; Kleinklaus, men; Boem, N; Granj, F; Giyom, J (2000). "Irsiy progressiv musinoz gistiotsitoz". Annales de Dermatologie va de Vénéréologie. 127 (4): 400–4. PMID  10844262.
  3. ^ Schlegel, C; Metzler, G; Burgdorf, Vt; Schaller, M (2010). "Irsiy progressiv musinozli gistiyotsitoz: erkak bemorda birinchi xabar". Acta Dermato Venereologica. 90 (1): 65–7. doi:10.2340/00015555-0763. PMID  20107728.



Tashqi havolalar

Tasnifi
Tashqi manbalar